Condylar hypoplasia is known as underdevelopment of the

mandibular condyle The condyloid process or condylar process is the process on the human and other mammalian species' mandibles that ends in a condyle, the mandibular condyle. It is thicker than the coronoid process of the mandible and consists of two portions: the ...

. Congenitally (primary) caused condylar hypoplasia leads to underdeveloped condyle at birth.

Hypoplasia Hypoplasia (; adjective form ''hypoplastic'') is underdevelopment or incomplete development of a tissue or organ.mandible In jawed vertebrates, the mandible (from the Latin ''mandibula'', 'for chewing'), lower jaw, or jawbone is a bone that makes up the lowerand typically more mobilecomponent of the mouth (the upper jaw being known as the maxilla). The jawbone i ...

can be diagnosed during birth, in comparison to the

hyperplasia Hyperplasia (from ancient Greek ὑπέρ ''huper'' 'over' + πλάσις ''plasis'' 'formation'), or hypergenesis, is an enlargement of an organ or tissue caused by an increase in the amount of Tissue (biology), organic tissue that results from ...

which is only diagnosed later in growth of an individual.

Types

Congenital (primary)

Congenital condylar hypoplasia happens when a person is born with smaller condyle than normal. The small condyle can be present either one or both sides of the lower jaw. This type of condition usually happens as part of systemic diseases such as

Hemifacial microsomia Hemifacial microsomia (HFM) is a congenital disorder that affects the development of the lower half of the face, most commonly the ears, the mouth and the mandible. It usually occurs on one side of the face, but both sides are sometimes affected. ...

, Mandibulofacial Dysostosis,

Goldenhar syndrome Goldenhar syndrome is a rare congenital defect characterized by incomplete development of the ear, nose, soft palate, lip and mandible on usually one side of the body. Common clinical manifestations include limbal dermoids, preauricular skin tag ...

Hurler syndrome Hurler syndrome, also known as mucopolysaccharidosis Type IH (MPS-IH), Hurler's disease, and formerly gargoylism, is a genetic disorder that results in the buildup of large sugar molecules called glycosaminoglycans (GAGs) in lysosomes. The inabil ...

Proteus syndrome Proteus syndrome is a rare genetic disorder that can cause tissue overgrowth involving all three Germ layer, embryonic lineages. Patients with Proteus syndrome tend to have an increased risk of embryonic tumor development.Freedberg, et al. (2003). ...

and

Morquio syndrome Morquio syndrome, also known as mucopolysaccharidosis type IV (MPS IV), is a rare metabolic disorder in which the body cannot process certain types of sugar molecules called glycosaminoglycans (AKA GAGs, or mucopolysaccharides). In Morquio syndro ...

Acquired (secondary)

Acquired condylar hypoplasia happens when a person is not born with a small condyle but they sustain an injury during their growth which leads to this condition. The injury causes stop of growth in the condyle, resulting in a smaller condyle. The type of injuries that can happen are most traumatic in nature. Injury or infection related to ear, childhood rheumatoid arthritis and parathyroid hormone related deficiency are known to cause the injury.

Presentation

Individuals with condylar hypoplasia may present with small mandible, symmetry in lower jaw and increased

overjet In dentistry, overjet is the extent of horizontal ( anterior-posterior) overlap of the maxillary central incisors over the mandibular central incisors. In class II (division I) malocclusion the overjet is increased as the maxillary central incis ...

. Depending on the presence or absence of the condyle, an individual may have limited opening of the mouth.

Diagnosis

Treatment

Treatment of this condyle usually requires a multi-team approach involving an oral surgeon, an orthodontist and a plastic surgeon. A treatment usually involves some type of bone graft from one's own body to their low jaw. A costochondral bone graft has been successfully used to add bone to the mandible by oral and plastic surgeons. This type of graft can be lengthened by a procedure known as

distraction osteogenesis Distraction osteogenesis (DO), also called callus distraction, callotasis and osteodistraction, is a process used in orthopedic surgery, podiatric surgery, and oral and maxillofacial surgery to repair skeletal deformities and in reconstructive su ...

which adds bone to the already placed graft. The graft is usually placed before the growth spurt occurs in an individual. The graft placement is later followed by an

orthognathic surgery Orthognathic surgery (), also known as corrective jaw surgery or simply jaw surgery, is surgery designed to correct conditions of the jaw and lower face related to structure, growth, airway issues including sleep apnea, TMJ disorders, malocclusio ...

after the growth has finished in an individual.

References

{{Reflist Orthodontics